What is a recommended dietary strategy for individuals with PKU?

Individuals with phenylketonuria (PKU) must adhere to a low-phenylalanine diet as a critical dietary strategy to manage their condition. PKU is a genetic disorder that affects the metabolism of phenylalanine, an amino acid found in many protein-rich foods. When people with PKU consume phenylalanine, it can accumulate in the body and lead to severe neurological damage and intellectual disabilities.

The low-phenylalanine diet involves restricting foods high in phenylalanine, such as meat, dairy, eggs, nuts, and soy products, while allowing for other foods that are either low in phenylalanine or specially formulated to be safe for individuals with PKU. This dietary management is essential to prevent the adverse effects associated with the excess of this amino acid.

Furthermore, individuals with PKU may utilize a special formula that provides protein without phenylalanine, ensuring they still receive adequate nutrition and maintain healthy growth and development. By carefully controlling dietary intake, individuals with PKU can lead healthy lives while minimizing the risks associated with the disorder.